A rare combination: chylous polyserositis and autoimmune myelofibrosis as a presentation of systemic lupus erythematosus.

Sir Ganga Ram Post-Graduate Institute Medical Education and Research (GRIPMER), New Delhi, India.Sir Ganga Ram Post-Graduate Institute Medical Education and Research (GRIPMER), New Delhi, India.Sir Ganga Ram Post-Graduate Institute Medical Education and Research (GRIPMER), New Delhi, India.

International journal of rheumatic diseases. 2019;(3):516-520

Abstract

Chylous polyserositis and autoimmune myelofibrosis occurring concomitantly inn a case of SLE are a rare phenomenon. We here report a case of a 38-year-old woman who was admitted with a history of cough and shortness of breath for 1½ months along with fever and abdominal distension for 1 month. She also had arthralgias, weight loss and pancytopenia. She was diagnosed as a case of SLE with Chylous polyserositis and autoimmune myelofibrosis. She was started on steroids and immunosuppressive therapy, to which she responded. To summarize, this is the first case report where chylous polyserositis and pancytopenia due to autoimmune myelofibrosis occurred which was responsive to steroids and immunosuppressive therapy.

Methodological quality

Publication Type : Case Reports ; Review

Metadata